%0 Generic
%A Cubides-Diaz D.A.
%A Lazaro V.N.
%A Rey M.
%A Mantilla K.
%A Cáceres E.
%8 2024
%U http://hdl.handle.net/10818/63346
%X Prion diseases are rare and rapidly progressive fatal neurological disorders characterized by abnormal folding of neuronal proteins. The diagnosis is often challenging and relies on a high clinical suspicion, imagenological findings, electroencephalographic (EEG) patterns and cerebrospinal fluid (CSF) analysis. We present a case of probable prion disease with an accelerated neurological decline and a non-convulsive status epilepticus (NCSE), which has only been described in a few cases worldwide, and seems to be associated with worse neurological outcomes and shorter survival time. Clinical manifestations, treatment, and outcomes are shown below. © 2024 Fundacion para la difusion neurologica en Ecuador - FUNDINE. All rights reserved.
%I Revista Ecuatoriana de Neurologia
%T Encephalitis and rapidly progressive dementia due to probable Prion disease presenting with a non-convulsive status epilepticus. Case report and literature review
%R 10.46997/revecuatneurol33100115
%~ Intellectum