%0 Generic
%A Coronado-Sarmiento J.F.
%A Coronado-López J.P.
%A Tuta-Quintero E.
%A Mora C.M.
%A Mayor V.
%8 2024
%@ 24593516
%U http://hdl.handle.net/10818/62766
%X Introduction: Eosinophilic granulomatosis with polyangiitis (eGPA) is a necrotising vasculitis of small and medium calibre vessels, which affects mostly patients in their fourth to sixth decade of life, and it is a very uncommon aetiology for pulmonary fibrosis. Clinical case: A Hispanic 72-year-old female patient presents with a history of lower extremities pain, paraesthesia, oedema, and occasional macroscopic haematuria. During her hospitalisation, the patient presents, and images showed findings compatible with pulmonary fibrosis and alveolar haemorrhage, which require a biopsy, establishing the diagnosis of an eGPA. Discussion: eGPA is a low-incidence autoimmune vasculitis, with a high number of phenotypes which explain the broad clinical spectrum, but recent advances has helped to understand the physiopathology and its link with other conditions like pulmonary fibrosis. Conclusion: Early diagnosis and management of this condition is mandatory because it is the only factor that change the outcome of the patients. © (2024), (Greek Rheumatology Society and Professional Association of Rheumatologists). All Rights Reserved.
%I Mediterranean Journal of Rheumatology
%T Late-Presenting Eosinophilic Granulomatosis with Polyangiitis as Cause of Pulmonary Fibrosis: A Case-Based Review
%R 10.31138/mjr.161023.lpe
%~ Intellectum