@misc{10818/63346, year = {2024}, url = {http://hdl.handle.net/10818/63346}, abstract = {Prion diseases are rare and rapidly progressive fatal neurological disorders characterized by abnormal folding of neuronal proteins. The diagnosis is often challenging and relies on a high clinical suspicion, imagenological findings, electroencephalographic (EEG) patterns and cerebrospinal fluid (CSF) analysis. We present a case of probable prion disease with an accelerated neurological decline and a non-convulsive status epilepticus (NCSE), which has only been described in a few cases worldwide, and seems to be associated with worse neurological outcomes and shorter survival time. Clinical manifestations, treatment, and outcomes are shown below. © 2024 Fundacion para la difusion neurologica en Ecuador - FUNDINE. All rights reserved.}, publisher = {Revista Ecuatoriana de Neurologia}, title = {Encephalitis and rapidly progressive dementia due to probable Prion disease presenting with a non-convulsive status epilepticus. Case report and literature review}, doi = {10.46997/revecuatneurol33100115}, author = {Cubides-Diaz D.A. and Lazaro V.N. and Rey M. and Mantilla K. and Cáceres E.}, }